Pediatric Neoplasms of the Pancreas: A Review
نویسنده
چکیده
In infants and children, pancreatic neoplasms occur uncommonly. Histologically, these tumors can resemble pancreatic embryonic elements or more well-differentiated pancreatic structures, in a subset the cellular origin can’t be delineated. This review discusses three of the most classic pediatric pancreatic neoplasms: pancreatoblastoma, solid pseudopapillary neoplasms and pancreatic endocrine neoplasms. These tumors can be a manifestation of a syndromic process and genetic aberrations have been linked to a subset of these neoplasms, as discussed in this paper.
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